Alveolar soft part sarcoma is a rare soft tissue tumor primarily within the skeletal muscles or musculofacial plane in young adults. Lung and brain are well known regions for late metastasis. Treatment modalities are surgery, radiotherapy and chemotherapy. Combination of surgery with radiotheraphy and chemotheraphy may prolong the mean survival time. Here we report a 32-year-old man presenting with an occipital mass. The patient was previously operated for masses on neck and left thigh with the same diagnosis. Histopathological specimens confirmed the diagnosis of alveolar soft part sarcoma metastatis. Despite systemic dissemination alveolar soft part sarcoma has a better prognosis if removed completely.

Keywords: Alveolar soft part sarcoma, cerebral metastasis, treatment